Anti-SGSH, CT (SGSH, HSS, N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase, Sulpham

Anti-SGSH, CT (SGSH, HSS, N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase, Sulpham
Item number Size Datasheet Manual SDS Delivery time Quantity Price
041675.200 200 µl - -

1 - 19 business days

557.00€
 
SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate.... more
Product information "Anti-SGSH, CT (SGSH, HSS, N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase, Sulpham"
SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. Applications: Suitable for use in ELISA and Western Blot. Other applications not tested. Recommended Dilutions: Western Blot: 1:4000, Optimal dilutions to be determined by the researcher. Storage and Stability: May be stored at 4°C for short-term only. Aliquot to avoid repeated freezing and thawing. Store at -20°C. Aliquots are stable for 12 months after receipt. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.
Keywords: Anti-HSS, Anti-SGSH, EC=3.10.1.1, Anti-Sulphamidase, Anti-Sulfoglucosamine sulfamidase, Anti-N-sulphoglucosamine sulphohydrolase
Supplier: United States Biological
Supplier-Nr: 041675

Properties

Application: ELISA, WB
Antibody Type: Polyclonal
Conjugate: No
Host: Rabbit
Reactivity: Human
Immunogen: SGSH antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 427~457 amino acids from the C-terminal region of human SGSH.
Format: Affinity Purified

Handling & Safety

Storage: -20°C
Shipping: +4°C (International: +4°C)
Caution
Our products are for laboratory research use only: Not for administration to humans!
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