Anti-Recombinant SPR, clone A748

Item number Size Datasheet Manual SDS Delivery time Quantity Price
E-AN302028L.50 50 µl -

7 - 16 business days*

304.00€
E-AN302028L.100 100 µl -

7 - 16 business days*

464.00€
 
SPR can catalyze the final one or two reductions in tetra-hydrobiopterin biosynthesis to form... more
Product information "Anti-Recombinant SPR, clone A748"
SPR can catalyze the final one or two reductions in tetra-hydrobiopterin biosynthesis to form 5,6,7,8-tetrahydrobiopterin.Defects in SPR are the cause of dystonia DOPA-responsive due to sepiapterin reductase deficiency (DRDSPRD). In the majority of cases, patients manifest progressive psychomotor retardation, dystonia and spasticity. Cognitive anomalies are also often present. The disease is due to severe dopamine and serotonin deficiencies in the central nervous system caused by a defect in BH4 synthesis.
Keywords: Anti-SPR, Anti-Sepiapterin reductase, Recombinant SPR Monoclonal Antibody
Supplier: Elabscience
Supplier-Nr: E-AN302028L

Properties

Application: WB, IHC
Antibody Type: Monoclonal
Clone: A748
Conjugate: No
Host: Rabbit
Species reactivity: human
Immunogen: Peptide. This information is proprietary to PTMab.
MW: 27 kD

Handling & Safety

Storage: -20°C
Shipping: -20°C (International: -20°C)
Signal Word: Warning
GHS Hazard Pictograms:
H Phrases: H317
P Phrases: P261, P272, P280, P302+352, P333+313
Caution
Our products are for laboratory research use only: Not for administration to humans!
You will get a certificate here
or to request a certificate of analysis.
Read, write and discuss reviews... more
Customer review for "Anti-Recombinant SPR, clone A748"
Write a review
or to review a product.
Viewed