Anti-GAA

Anti-GAA
Item number Size Datasheet Manual SDS Delivery time Quantity Price
E-AB-65554.60 60 µl -

7 - 16 business days*

198.00€
E-AB-65554.120 120 µl -

7 - 16 business days*

317.00€
E-AB-65554.200 200 µl -

7 - 16 business days*

525.00€
 
This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen... more
Product information "Anti-GAA"
This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. Protein function: Essential for the degradation of glycogen in lysosomes (PubMed:1856189, PubMed:7717400, PubMed:14695532, PubMed:18429042). Has highest activity on alpha-1,4-linked glycosidic linkages, but can also hydrolyze alpha-1,6-linked glucans (PubMed:29061980). [The UniProt Consortium]
Keywords: Anti-GAA, GAA Polyclonal Antibody
Supplier: Elabscience
Supplier-Nr: E-AB-65554

Properties

Application: WB
Antibody Type: Polyclonal
Conjugate: No
Host: Rabbit
Species reactivity: human, mouse, rat
Immunogen: A synthetic peptide of human GAA

Handling & Safety

Storage: -20°C
Shipping: 4°C (International: -20°C)
Caution
Our products are for laboratory research use only: Not for administration to humans!
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