Anti-PAH / Phenylalanine hydroxylase

0.5mg/ml if reconstituted with 0.2ml sterile DI water. Phenylalanine hydroxylase (PAH) is an enzyme that catalyzes the hydroxylation of the aromatic side-chain of phenylalanine to generate tyrosine. It is one of three members of the biopterin-dependent aromatic amino acid hydroxylases, a class of monooxygenase that uses tetrahydrobiopterin (BH4, a pteridine cofactor) and a non-heme iron for catalysis. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria. Protein function: Catalyzes the hydroxylation of L-phenylalanine to L-tyrosine. [The UniProt Consortium]