- Search results for P00480
Cookie preferences
This website uses cookies, which are necessary for the technical operation of the website and are always set. Other cookies, which increase the comfort when using this website, are used for direct advertising or to facilitate interaction with other websites and social networks, are only set with your consent.
Configuration
Technically required
These cookies are necessary for the basic functions of the shop.
"Allow all cookies" cookie
"Decline all cookies" cookie
CSRF token
Cookie preferences
Currency change
Customer-specific caching
FACT-Finder tracking
Individual prices
Selected shop
Session
Comfort functions
These cookies are used to make the shopping experience even more appealing, for example for the recognition of the visitor.
Note
Show the facebook fanpage in the right blod sidebar
Statistics & Tracking
Affiliate program
Conversion and usertracking via Google Tag Manager
Track device being used
37 products were found matching "P00480"!
Close filters
Filter by:
No results were found for the filter!
Item number: G-HUFI01383.96
| Application: | ELISA |
| Species reactivity: | human |
698.00€
*
Item number: E-AB-15274.120
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.
| Keywords: | Anti-OTC, Anti-OTCase, EC=2.1.3.3, Anti-Ornithine transcarbamylase, Anti-Ornithine carbamoyltransferase, mitochondrial,... |
| Application: | WB, IHC, ELISA |
| Host: | Rabbit |
| Species reactivity: | human, mouse, rat |
From 89.00€
*
Item number: E-AB-11461.120
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.
| Keywords: | Anti-OTC, Anti-OTCase, EC=2.1.3.3, Anti-Ornithine transcarbamylase, Anti-Ornithine carbamoyltransferase, mitochondrial,... |
| Application: | WB, IHC, ELISA |
| Host: | Rabbit |
| Species reactivity: | human, mouse, rat |
From 89.00€
*
Item number: ARG58979.100
| Keywords: | Anti-OTC, Anti-OTCase, EC=2.1.3.3, Anti-Ornithine transcarbamylase, Anti-Ornithine carbamoyltransferase, mitochondrial |
| Application: | WB |
| Host: | Rabbit |
| Species reactivity: | mouse, rat |
707.00€
*
Item number: ARG58999.100
| Keywords: | Anti-OTC, Anti-OTCase, EC=2.1.3.3, Anti-Ornithine transcarbamylase, Anti-Ornithine carbamoyltransferase, mitochondrial |
| Application: | IHC (paraffin), WB |
| Host: | Rabbit |
| Species reactivity: | human |
616.00€
*
Item number: G-HUES02748.96
ELISA Type: Sandwich. Sensitivity: 0.281ng/mL. Range: 0.469--30ng/mL. 0
| Keywords: | OTC, OTCase, EC=2.1.3.3, Ornithine transcarbamylase, Ornithine carbamoyltransferase, mitochondrial |
| Application: | Sandwich ELISA |
| Species reactivity: | human |
708.00€
*
Item number: ATA-AMAb91264.100
Protein function: Catalyzes the second step of the urea cycle, the condensation of carbamoyl phosphate with L-ornithine to form L-citrulline (PubMed:6372096, PubMed:8112735, PubMed:2556444). The urea cycle ensures the detoxification of ammonia by converting it to urea for excretion (PubMed:2556444). [The UniProt...
| Keywords: | Anti-OTCase, Anti-Ornithine transcarbamylase, mitochondrial, Anti-Ornithine carbamoyltransferase, mitochondrial |
| Application: | ICC, IHC, WB |
| Host: | Mouse |
| Species reactivity: | human |
From 330.00€
*
Item number: ATA-AMAb91265.100
Protein function: Catalyzes the second step of the urea cycle, the condensation of carbamoyl phosphate with L-ornithine to form L-citrulline (PubMed:6372096, PubMed:8112735, PubMed:2556444). The urea cycle ensures the detoxification of ammonia by converting it to urea for excretion (PubMed:2556444). [The UniProt...
| Keywords: | Anti-OTCase, Anti-Ornithine transcarbamylase, mitochondrial, Anti-Ornithine carbamoyltransferase, mitochondrial |
| Application: | ICC, IHC, WB |
| Host: | Mouse |
| Species reactivity: | human |
From 330.00€
*
Item number: ATA-AMAb91266.100
Protein function: Catalyzes the second step of the urea cycle, the condensation of carbamoyl phosphate with L-ornithine to form L-citrulline (PubMed:6372096, PubMed:8112735, PubMed:2556444). The urea cycle ensures the detoxification of ammonia by converting it to urea for excretion (PubMed:2556444). [The UniProt...
| Keywords: | Anti-OTCase, Anti-Ornithine transcarbamylase, mitochondrial, Anti-Ornithine carbamoyltransferase, mitochondrial |
| Application: | WB |
| Host: | Mouse |
| Species reactivity: | human |
From 330.00€
*
Item number: ATA-HPA000243.100
Protein function: Catalyzes the second step of the urea cycle, the condensation of carbamoyl phosphate with L-ornithine to form L-citrulline (PubMed:6372096, PubMed:8112735, PubMed:2556444). The urea cycle ensures the detoxification of ammonia by converting it to urea for excretion (PubMed:2556444). [The UniProt...
| Keywords: | Anti-OTCase, Anti-Ornithine transcarbamylase, mitochondrial, Anti-Ornithine carbamoyltransferase, mitochondrial |
| Application: | WB, IHC, ICC |
| Host: | Rabbit |
| Species reactivity: | human |
From 330.00€
*
Item number: ATA-HPA000570.100
Protein function: Catalyzes the second step of the urea cycle, the condensation of carbamoyl phosphate with L-ornithine to form L-citrulline (PubMed:6372096, PubMed:8112735, PubMed:2556444). The urea cycle ensures the detoxification of ammonia by converting it to urea for excretion (PubMed:2556444). [The UniProt...
| Keywords: | Anti-OTCase, Anti-Ornithine transcarbamylase, mitochondrial, Anti-Ornithine carbamoyltransferase, mitochondrial |
| Application: | IHC |
| Host: | Rabbit |
| Species reactivity: | human |
From 330.00€
*
Item number: CSB-EP017270HU.1
Organism: Homo sapiens (Human). Source: E.coli. Expression Region: 33-354aa. Protein Length: Full Length of Mature Protein. Tag Info: N-terminal 6xHis-SUMO-tagged. Target Protein Sequence: NKVQLKGRDL LTLKNFTGEE IKYMLWLSAD LKFRIKQKGE YLPLLQGKSL GMIFEKRSTR TRLSTETGFA LLGGHPCFLT TQDIHLGVNE SLTDTARVLS SMADAVLARV...
| Keywords: | OTCase, Ornithine transcarbamylase, mitochondrial, Ornithine carbamoyltransferase, mitochondrial, Recombinant Human... |
| Application: | Activity not tested |
| Expressed in: | E.coli |
| Origin: | human |
| MW: | 52.1 kD |
From 219.00€
*