50 products were found matching "K01189"!

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Alpha-galactosidase A (GLA), human, recombinant
Alpha-galactosidase A (GLA), human, recombinant

Item number: CSB-EP009474HU.1

Organism: Homo sapiens (Human). Source: E.coli. Expression Region: 32-429aa. Protein Length: Full Length of Mature Protein. Tag Info: N-terminal 6xHis-tagged. Target Protein Sequence: LDNGLARTPT MGWLHWERFM CNLDCQEEPD SCISEKLFME MAELMVSEGW KDAGYEYLCI DDCWMAPQRD SEGRLQADPQ RFPHGIRQLA NYVHSKGLKL GIYADVGNKT CAGFPGSFGY...
Keywords: Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase,...
Application: Activity not tested
Expressed in: E.coli
Origin: human
MW: 49.4 kD
From 213.00€ *
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Anti-GLA Recombinant Monoclonal, clone 30H11
Anti-GLA Recombinant Monoclonal, clone 30H11

Item number: CSB-RA950991A0HU.100

Isotype: Rabbit IgG. Buffer: Rabbit IgG in phosphate buffered saline, pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol. Storage: Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. Purification Method: Affinity-chromatography. Target Name: GLA. Antigen Species: Human
Keywords: Anti-Melibiase, Anti-Agalsidase, Anti-Alpha-galactosidase A, Anti-Alpha-D-galactosidase A, Anti-Alpha-D-galactoside...
Application: ELISA, IHC, FC
Host: Rabbit
Species reactivity: human
From 201.00€ *
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alpha-Galactosidase (alpha-Gal) Acitivity Assay Kit
alpha-Galactosidase (alpha-Gal) Acitivity Assay Kit

Item number: E-BC-K630-M.96

Detection principle: alpha-Galactosidase (alpha-Gal) catalyzes the substances produced in the glycolysis process of animal and plant tissues to form the final product, which has a maximum absorption peak at 405 nm. Performance characteristics: Sample type: animal tissue,plant tissue. Sensitivity: 0.02 U/L. Detection...
Keywords: Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase,...
356.00€ *
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Human GLa (Galactosidase Alpha) ELISA Kit
Human GLa (Galactosidase Alpha) ELISA Kit

Item number: ELK-ELK2860.48

The test principle applied in this kit is Sandwich enzyme immunoassay. The microtiter plate provided in this kit has been pre-coated with an antibody specific to Human GLa. Standards or samples are added to the appropriate microtiter plate wells then with a biotin-conjugated antibody specific to Human GLa. Next,...
Keywords: Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase,...
Application: ELISA
Species reactivity: human
From 365.00€ *
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N-(n-Butyl)deoxygalactonojirimycin
N-(n-Butyl)deoxygalactonojirimycin

Item number: Cay19520-5

N-(n-Butyl)deoxygalactonojirimycin (NB-DGJ) is an inhibitor of the glycolipid biosynthesis enzyme glucosylceramide synthase and the glycolipid catabolic enzymes glucocerebrosidase (GBA) and beta-glucosidase 2 (GBA2). It also inhibits acid alpha-glucosidase, sucrase, maltase, and lactase. NB-DGJ (0.5-500 µM) reduces...
Keywords: Lucerastat, NBDGJ, 1-butyl-2R-(hydroxymethyl)-3S,4R,5S-piperidinetriol
Application: alpha-D-galactosidase inhibitor
CAS 141206-42-0
MW: 219.3 D
From 60.00€ *
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1-Deoxygalactonojirimycin (hydrochloride)
1-Deoxygalactonojirimycin (hydrochloride)

Item number: Cay17179-5

1-Deoxygalactonojirimycin is a competititve inhibitor of alpha-galactosidase (IC50 = 40 nM). At subinhibitory concentrations, 1-Deoxygalactonojirimycin binds to alpha-galactosidase and chaperones unstable enzyme variants through the endoplasmic reticulum, allowing its movement into lysosomes. Pharmacological...
Keywords: DGJ, Migalastat, (2R,3S,4R,5S)-2-(hydroxymethyl)-3,4,5-piperidinetriol, monohydrochloride
Application: alpha-galactosidase inhibitor
CAS 75172-81-5
MW: 199.6 D
From 52.00€ *
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D-(+)-Raffinose (hydrate)
D-(+)-Raffinose (hydrate)

Item number: Cay16773-10

D-(+)-Raffinose is a trisaccharide composed of galactose, glucose, and fructose that occurs naturally in a variety of vegetables and grains. It is hydrolyzed to galactose and sucrose by alpha-galactosidase.Formal Name: beta-D-fructofuranosyl O-alpha-D-galactopyranosyl-(1->6)-alpha-D-glucopyranoside, pentahydrate....
Keywords: beta-D-fructofuranosyl O-alpha-D-galactopyranosyl-(1->6)-alpha-D-glucopyranoside, pentahydrate
Application: Trisaccharide
CAS 17629-30-0
MW: 594.5 D
From 42.00€ *
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4-Methylumbelliferyl-alpha-D-Galactopyranoside
4-Methylumbelliferyl-alpha-D-Galactopyranoside

Item number: Cay16551-25

4-Methylumbelliferyl-alpha-D-galactopyranoside (4-MU-alpha-Gal) is a fluorogenic substrate of alpha-galactosidase. In addition to its use in characterizing novel alpha-galactosidases, 4-MU-alpha-Gal is used in assays to evaluate deficiency in alpha-galactosidase activity related to Fabry disease. Hydrolysis of...
Keywords: 4-MU-alpha-Gal, MU-alpha-Gal, 7-(alpha-D-galactopyranosyloxy)-4-methyl-2H-1-benzopyran-2-one
Application: Fluorogenic alpha-galactosidase substrate
CAS 38597-12-5
MW: 338.3 D
From 43.00€ *
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Human GLA / Alpha-galactosidase A ELISA Kit
Human GLA / Alpha-galactosidase A ELISA Kit

Item number: G-HUFI00532.96

Application: ELISA
Species reactivity: human
534.00€ *
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Human GLalpha (Galactosidase Alpha) ELISA Kit
Human GLalpha (Galactosidase Alpha) ELISA Kit

Item number: E-EL-H0972.96

The kit is a Sandwich enzyme immunoassay for in vitro quantitative measurement of GLalpha in serum, plasma and other biological fluids. Detection Range: 78.13--5000pg/mL. Sensitivity: 46.88pg/mL.
Keywords: GLA, Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase
Application: ELISA
Species reactivity: human
483.00€ *
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-30 %
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Anti-Galactosidase alpha
Anti-Galactosidase alpha

Item number: ARG58844.100

Keywords: Anti-GLA, Anti-Melibiase, Anti-Agalsidase, Anti-Alpha-galactosidase A, Anti-Alpha-D-galactosidase A,...
Application: ICC, IF, IHC (paraffin)
Host: Rabbit
Species reactivity: human, mouse
624.00€ * 436.80€ *
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Human GL alpha (Galactosidase Alpha) CLIA Kit
Human GL alpha (Galactosidase Alpha) CLIA Kit

Item number: G-HUES00578.96

ELISA Type: CLIA. Sensitivity: 9.375 pg/mL. Range: 15.625--1000 pg/mL. 0
Keywords: GLA, Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase
Application: CLIA
Species reactivity: human
694.00€ *
Review
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