61 products were found matching "K01189"!
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Anti-GLalpha/Galactosidase Alpha
Item number: E-AN006790L.100
alpha -Galactosidase A is a homodimeric glycoprotein that can release terminal alpha -galactosyl moieties from glycolipids and glycoproteins and catalyze the hydrolysis of melibiose into galactose and glucose . It is a lysosomal enzyme and is responsible for degradation of glycolipid globotriaosylceramide (Gb3) (Gal...
| Keywords: | Anti-GLA, Anti-Melibiase, Anti-Alpha-galactosidase A, Anti-Alpha-D-galactosidase A, Anti-Alpha-D-galactoside... |
| Application: | WB, IHC |
| Host: | Rabbit |
| Species reactivity: | human |
From 110.00€
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Human Galactosidase alpha ELISA Kit
Item number: ARG82609.96
| Keywords: | GLA, Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase |
| Application: | ELISA |
| Species reactivity: | human |
912.00€
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N-(n-Butyl)deoxygalactonojirimycin
Item number: Cay19520-5
N-(n-Butyl)deoxygalactonojirimycin (NB-DGJ) is an inhibitor of the glycolipid biosynthesis enzyme glucosylceramide synthase and the glycolipid catabolic enzymes glucocerebrosidase (GBA) and beta-glucosidase 2 (GBA2). It also inhibits acid alpha-glucosidase, sucrase, maltase, and lactase. NB-DGJ (0.5-500 µM) reduces...
| Keywords: | Lucerastat, NBDGJ, 1-butyl-2R-(hydroxymethyl)-3S,4R,5S-piperidinetriol |
| Application: | alpha-D-galactosidase inhibitor |
| CAS | 141206-42-0 |
| MW: | 219.3 D |
From 67.00€
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GLA (human), recombinant protein (His Tag)
Item number: E-PDMH100451.1
Protein function: Catalyzes the hydrolysis of glycosphingolipids and participates in their degradation in the lysosome. [The UniProt Consortium]
| Keywords: | Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase,... |
| Expressed in: | Mammalian |
| Origin: | human |
From 192.00€
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1-Deoxygalactonojirimycin (hydrochloride)
Item number: Cay17179-5
1-Deoxygalactonojirimycin is a competititve inhibitor of alpha-galactosidase (IC50 = 40 nM). At subinhibitory concentrations, 1-Deoxygalactonojirimycin binds to alpha-galactosidase and chaperones unstable enzyme variants through the endoplasmic reticulum, allowing its movement into lysosomes. Pharmacological...
| Keywords: | DGJ, Migalastat, (2R,3S,4R,5S)-2-(hydroxymethyl)-3,4,5-piperidinetriol, monohydrochloride |
| Application: | alpha-galactosidase inhibitor |
| CAS | 75172-81-5 |
| MW: | 199.6 D |
From 57.00€
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X-alpha-Gal
Item number: Cay36095-100
X-alpha-Gal is a chromogenic substrate for alpha-galactosidase. Upon cleavage by alpha-galactosidase, a blue pigment is released that can be used as a marker of alpha-galactosidase activity. X-alpha-Gal has been used in the identification of S. cerevisiae and S. bayanus hybrid yeast.Formal Name:...
| Keywords: | 5-bromo-4-chloro-3-indolyl-alpha-D-Galactopyranoside, 5-bromo-4-chloro-1H-indol-3-yl alpha-D-galactopyranoside |
| Application: | Chromogenic alpha-galactosidase substrate |
| CAS | 107021-38-5 |
| MW: | 408.6 D |
From 84.00€
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4-Methylumbelliferyl-alpha-D-Galactopyranoside
Item number: Cay16551-100
4-Methylumbelliferyl-alpha-D-galactopyranoside (4-MU-alpha-Gal) is a fluorogenic substrate of alpha-galactosidase. In addition to its use in characterizing novel alpha-galactosidases, 4-MU-alpha-Gal is used in assays to evaluate deficiency in alpha-galactosidase activity related to Fabry disease. Hydrolysis of...
| Keywords: | 4-MU-alpha-Gal, MU-alpha-Gal, 7-(alpha-D-galactopyranosyloxy)-4-methyl-2H-1-benzopyran-2-one |
| Application: | Fluorogenic alpha-galactosidase substrate |
| CAS | 38597-12-5 |
| MW: | 338.3 D |
From 58.00€
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D-(+)-Raffinose (hydrate)
Item number: Cay16773-10
D-(+)-Raffinose is a trisaccharide composed of galactose, glucose, and fructose that occurs naturally in a variety of vegetables and grains. It is hydrolyzed to galactose and sucrose by alpha-galactosidase.Formal Name: beta-D-fructofuranosyl O-alpha-D-galactopyranosyl-(1->6)-alpha-D-glucopyranoside, pentahydrate....
| Keywords: | beta-D-fructofuranosyl O-alpha-D-galactopyranosyl-(1->6)-alpha-D-glucopyranoside, pentahydrate |
| Application: | Trisaccharide |
| CAS | 17629-30-0 |
| MW: | 594.5 D |
From 48.00€
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4-Methylumbelliferyl-alpha-D-Galactopyranoside
Item number: TGM-T37192-50mg
Description: 4-Methylumbelliferyl-alpha-D-Galactopyranoside (4MU-alpha-Gal) (4-MU-alpha-Gal) is a fluorogenic substrate of alpha-galactosidase. In addition to its use in characterizing novel alpha-galactosidases, 4-MU-alpha-Gal is used in assays to evaluate deficiency in alpha-galactosidase activity related to Fabry...
| Keywords: | 4MU-alpha-Gal |
| Application: | Fluorogenic alpha-galactosidase substrate |
| CAS | 38597-12-5 |
| MW: | 338.31 D |
From 34.00€
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Human GLA / Alpha-galactosidase A ELISA Kit
Item number: G-HUFI00532.96
| Application: | ELISA |
| Species reactivity: | human |
644.00€
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Anti-Galactosidase alpha
Item number: ARG58844.100
| Keywords: | Anti-GLA, Anti-Melibiase, Anti-Agalsidase, Anti-Alpha-galactosidase A, Anti-Alpha-D-galactosidase A,... |
| Application: | ICC, IF, IHC (paraffin) |
| Host: | Rabbit |
| Species reactivity: | human, mouse |
707.00€
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Human GL alpha (Galactosidase Alpha) ELISA Kit
Item number: G-HUES02093.96
ELISA Type: Sandwich. Sensitivity: 46.875pg/mL. Range: 78.125--5000pg/mL. 0
| Keywords: | GLA, Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase |
| Application: | Sandwich ELISA |
| Species reactivity: | human |
708.00€
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