Isobutyryl-L-carnitine-d3 (chloride)

Isobutyryl-L-carnitine-d3 is intended for use as an internal standard for the quantification of isobutyryl-L-carnitine by GC- or LC-MS. Isobutyryl-L-carnitine is a natural 4-carbon acylcarnitine that is involved in fatty acid oxidation and organic acid metabolism. Elevated levels of isobutyryl-L-carnitine are associated with isobutyryl-CoA dehydrogenase deficiency.Formal Name: (R)-3-carboxy-2-(isobutyryloxy)-N,N-dimethyl-N-(methyl-d3)propan-1-aminium, monochloride. Synonyms: CAR 4:0-d3, C4:0 Carnitine-d3, L-Carnitine isobutyryl ester-d3, L-Isobutyrylcarnitine-d3. Molecular Formula: C11H19D3NO4 . Cl. Formula Weight: 270.8. Purity: >99% deuterated forms (d1-d3). Formulation: (Request formulation change), A crystalline solid. Solubility: DMF: 20 mg/ml, DMSO: 20 mg/ml, Ethanol: 25 mg/ml, PBS (pH 7.2): 10 mg/ml. SMILES: OC(C[C@@H](OC(C(C)C)=O)C[N+](C)(C)C([2H])([2H])[2H])=O.[Cl-]. InChi Code: InChI=1S/C11H21NO4.ClH/c1-8(2)11(15)16-9(6-10(13)14)7-12(3,4)5,/h8-9H,6-7H2,1-5H3,1H/t9-,/m1./s1/i3D3,. InChi Key: FWUACOYFRJEMMP-WINMCZQPSA-N.