Heptadecanoyl-L-carnitine-d3 (chloride)

Heptadecanoyl-L-carnitine-d3 is intended for use as an internal standard for the quantification of heptadecanoyl-L-carnitine by GC- or LC-MS. Heptadecanoyl-L-carnitine is a long-chain acylcarnitine composed of heptadecanoic acid (Cay-19722) and L-carnitine (Cay-21489). Levels of heptadecanoyl-L-carnitine are increased in dried blood spots from neonates with propionic or methylmalonic acidemias, inborn errors of metabolism characterized by a deficiency in the activity of propionyl-CoA carboxylase or L-methylmalonyl-CoA mutase or its cofactor 5-deoxyadenosylcobalamin, respectively.Formal Name: (R)-3-carboxy-2-(heptadecanoyloxy)-N,N-dimethyl-N-(methyl-d3)propan-1-aminium, monochloride. Synonyms: CAR 17:0-d3, C17:0 Carnitine-d3, L-Carnitine heptadecanoyl ester-d3, L-Heptadecanoylcarnitine-d3. Molecular Formula: C24H45D3NO4 . Cl. Formula Weight: 453.1. Purity: >95%. Formulation: (Request formulation change), A crystalline solid. Solubility: DMF: 20 mg/ml, DMSO: 14 mg/ml, Ethanol: 10 mg/ml. SMILES: C[N+](C([2H])([2H])[2H])(C)C[C@@H](CC(O)=O)OC(CCCCCCCCCCCCCCCC)=O.[Cl-]. InChi Code: InChI=1S/C24H47NO4.ClH/c1-5-6-7-8-9-10-11-12-13-14-15-16-17-18-19-24(28)29-22(20-23(26)27)21-25(2,3)4,/h22H,5-21H2,1-4H3,1H/t22-,/m1./s1/i2D3,. InChi Key: SYUSIANKHPXISE-SZCCLSIUSA-N.