L-Carnitine hydrochloride

Description: Carnitine is a quaternary amine that occurs naturally in most mammalian tissue. Carnitine is present in relatively high concentrations in skeletal muscle and heart where it is involved in regulating energy metabolism. It has also been used to allow the entry of palmitic acid into the mitochondria. Target: Others. Smiles: [Cl-].C[N+](C)(C)C[C@H](O)CC(O)=O. References: Nunes V, Niinikoski H. Lysinuric Protein Intolerance. 2006 Dec 21 [updated 2018 Apr 12]. In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Stephens K, Amemiya A, editors. GeneReviews(R) [Internet]. Seattle (WA): University of Washington, Seattle, 1993-2018. Available from http://www.ncbi.nlm.nih.gov/books/NBK1361/ PubMed PMID: 20301535.