Anti-PMPCB

This gene is a member of the peptidase M16 family and encodes a protein with a zinc-binding motif. This protein is located in the mitochondrial matrix and catalyzes the cleavage of the leader peptides of precursor proteins newly imported into the mitochondria, though it only functions as part of a heterodimeric complex. Protein function: Cleaves presequences (transit peptides) from mitochondrial protein precursors. [The UniProt Consortium]