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Anti-GLalpha/Galactosidase Alpha
Anti-GLalpha/Galactosidase Alpha

Artikelnummer: E-AN006790L.100

alpha -Galactosidase A is a homodimeric glycoprotein that can release terminal alpha -galactosyl moieties from glycolipids and glycoproteins and catalyze the hydrolysis of melibiose into galactose and glucose . It is a lysosomal enzyme and is responsible for degradation of glycolipid globotriaosylceramide (Gb3) (Gal...
Schlagworte: Anti-GLA, Anti-Melibiase, Anti-Alpha-galactosidase A, Anti-Alpha-D-galactosidase A, Anti-Alpha-D-galactoside...
Anwendung: WB, IHC
Wirt: Rabbit
Spezies-Reaktivität: human
ab 110,00 €
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Human Galactosidase alpha ELISA Kit
Human Galactosidase alpha ELISA Kit

Artikelnummer: ARG82609.96

Schlagworte: GLA, Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase
Anwendung: ELISA
Spezies-Reaktivität: human
912,00 €
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N-(n-Butyl)deoxygalactonojirimycin
N-(n-Butyl)deoxygalactonojirimycin

Artikelnummer: Cay19520-5

N-(n-Butyl)deoxygalactonojirimycin (NB-DGJ) is an inhibitor of the glycolipid biosynthesis enzyme glucosylceramide synthase and the glycolipid catabolic enzymes glucocerebrosidase (GBA) and beta-glucosidase 2 (GBA2). It also inhibits acid alpha-glucosidase, sucrase, maltase, and lactase. NB-DGJ (0.5-500 µM) reduces...
Schlagworte: Lucerastat, NBDGJ, 1-butyl-2R-(hydroxymethyl)-3S,4R,5S-piperidinetriol
Anwendung: alpha-D-galactosidase inhibitor
CAS 141206-42-0
MW: 219.3 D
ab 67,00 €
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GLA (human), recombinant protein (His Tag)
GLA (human), recombinant protein (His Tag)

Artikelnummer: E-PDMH100451.1

Protein function: Catalyzes the hydrolysis of glycosphingolipids and participates in their degradation in the lysosome. [The UniProt Consortium]
Schlagworte: Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase,...
Exprimiert in: Mammalian
Ursprungsart: human
ab 192,00 €
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1-Deoxygalactonojirimycin (hydrochloride)
1-Deoxygalactonojirimycin (hydrochloride)

Artikelnummer: Cay17179-5

1-Deoxygalactonojirimycin is a competititve inhibitor of alpha-galactosidase (IC50 = 40 nM). At subinhibitory concentrations, 1-Deoxygalactonojirimycin binds to alpha-galactosidase and chaperones unstable enzyme variants through the endoplasmic reticulum, allowing its movement into lysosomes. Pharmacological...
Schlagworte: DGJ, Migalastat, (2R,3S,4R,5S)-2-(hydroxymethyl)-3,4,5-piperidinetriol, monohydrochloride
Anwendung: alpha-galactosidase inhibitor
CAS 75172-81-5
MW: 199.6 D
ab 57,00 €
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X-alpha-Gal
X-alpha-Gal

Artikelnummer: Cay36095-100

X-alpha-Gal is a chromogenic substrate for alpha-galactosidase. Upon cleavage by alpha-galactosidase, a blue pigment is released that can be used as a marker of alpha-galactosidase activity. X-alpha-Gal has been used in the identification of S. cerevisiae and S. bayanus hybrid yeast.Formal Name:...
Schlagworte: 5-bromo-4-chloro-3-indolyl-alpha-D-Galactopyranoside, 5-bromo-4-chloro-1H-indol-3-yl alpha-D-galactopyranoside
Anwendung: Chromogenic alpha-galactosidase substrate
CAS 107021-38-5
MW: 408.6 D
ab 84,00 €
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4-Methylumbelliferyl-alpha-D-Galactopyranoside
4-Methylumbelliferyl-alpha-D-Galactopyranoside

Artikelnummer: Cay16551-100

4-Methylumbelliferyl-alpha-D-galactopyranoside (4-MU-alpha-Gal) is a fluorogenic substrate of alpha-galactosidase. In addition to its use in characterizing novel alpha-galactosidases, 4-MU-alpha-Gal is used in assays to evaluate deficiency in alpha-galactosidase activity related to Fabry disease. Hydrolysis of...
Schlagworte: 4-MU-alpha-Gal, MU-alpha-Gal, 7-(alpha-D-galactopyranosyloxy)-4-methyl-2H-1-benzopyran-2-one
Anwendung: Fluorogenic alpha-galactosidase substrate
CAS 38597-12-5
MW: 338.3 D
ab 58,00 €
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D-(+)-Raffinose (hydrate)
D-(+)-Raffinose (hydrate)

Artikelnummer: Cay16773-10

D-(+)-Raffinose is a trisaccharide composed of galactose, glucose, and fructose that occurs naturally in a variety of vegetables and grains. It is hydrolyzed to galactose and sucrose by alpha-galactosidase.Formal Name: beta-D-fructofuranosyl O-alpha-D-galactopyranosyl-(1->6)-alpha-D-glucopyranoside, pentahydrate....
Schlagworte: beta-D-fructofuranosyl O-alpha-D-galactopyranosyl-(1->6)-alpha-D-glucopyranoside, pentahydrate
Anwendung: Trisaccharide
CAS 17629-30-0
MW: 594.5 D
ab 48,00 €
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4-Methylumbelliferyl-alpha-D-Galactopyranoside
4-Methylumbelliferyl-alpha-D-Galactopyranoside

Artikelnummer: TGM-T37192-50mg

Description: 4-Methylumbelliferyl-alpha-D-Galactopyranoside (4MU-alpha-Gal) (4-MU-alpha-Gal) is a fluorogenic substrate of alpha-galactosidase. In addition to its use in characterizing novel alpha-galactosidases, 4-MU-alpha-Gal is used in assays to evaluate deficiency in alpha-galactosidase activity related to Fabry...
Schlagworte: 4MU-alpha-Gal
Anwendung: Fluorogenic alpha-galactosidase substrate
CAS 38597-12-5
MW: 338.31 D
ab 34,00 €
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Human GLA / Alpha-galactosidase A ELISA Kit
Human GLA / Alpha-galactosidase A ELISA Kit

Artikelnummer: G-HUFI00532.96

Anwendung: ELISA
Spezies-Reaktivität: human
644,00 €
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Anti-Galactosidase alpha
Anti-Galactosidase alpha

Artikelnummer: ARG58844.100

Schlagworte: Anti-GLA, Anti-Melibiase, Anti-Agalsidase, Anti-Alpha-galactosidase A, Anti-Alpha-D-galactosidase A,...
Anwendung: ICC, IF, IHC (paraffin)
Wirt: Rabbit
Spezies-Reaktivität: human, mouse
707,00 €
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Human GL alpha (Galactosidase Alpha) ELISA Kit
Human GL alpha (Galactosidase Alpha) ELISA Kit

Artikelnummer: G-HUES02093.96

ELISA Type: Sandwich. Sensitivity: 46.875pg/mL. Range: 78.125--5000pg/mL. 0
Schlagworte: GLA, Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase
Anwendung: Sandwich ELISA
Spezies-Reaktivität: human
708,00 €
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