Zu "K00253" wurden 30 Artikel gefunden!
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Anti-Isovaleryl-CoA dehydrogenase/IVD Monoclonal Antibody
Artikelnummer: E-AN200143P.100
Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript...
| Schlagworte: | IVD, Butyryl-CoA dehydrogenase, Isovaleryl-CoA dehydrogenase, mitochondrial, Isovaleryl-CoA dehydrogenase/IVD Monoclonal... |
| Anwendung: | WB, FCM, ICC/IF, IP |
| Wirt: | Mouse |
| Spezies-Reaktivität: | human |
389,00 €
Isovaleroylglycine
Artikelnummer: Cay17581-500
Isovaleroylglycine is a compound found in the urine of patients with isovaleric acidemia, a disorder created by defective leucine metabolism due to a deficiency in the isovaleryl coenzyme A dehydrogenase. It has been used as a diagnostic tool in the diagnosis of various acidemias and mitochondrial fatty acid...
| Schlagworte: | N-Isovalerylglycine, N-(3-methyl-1-oxobutyl)-glycine |
| CAS | 16284-60-9 |
| MW: | 159.2 D |
ab 67,00 €
Isovaleryl-DL-carnitine-d3 (chloride)
Artikelnummer: Cay26573-1
Isovaleryl-DL-carnitine-d3 is intended for use as an internal standard for the quantification of isovaleryl-DL-carnitine by GC- or LC-MS. Isovaleryl-DL-carnitine is a derivative of carnitine (Cay-21489, Cay-16749). Increased levels of isovaleryl carnitine are associated with isovaleric acidemia, an inborn error of...
| Schlagworte: | DL-Isovalerylcarnitine-d3, 3-carboxy-N,N-dimethyl-N-(methyl-d3)-2-((3-methylbutanoyl)oxy)propan-1-aminium, monochloride |
| Anwendung: | GC-MS, LC-MS, quantification, internal standard, isovaleryl-CoA dehydrogenase defiency marker |
| MW: | 278.7 D |
ab 102,00 €
Anti-IVD
Artikelnummer: ARG58891.100
| Schlagworte: | Anti-IVD, EC=1.3.8.4, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial |
| Anwendung: | WB |
| Wirt: | Rabbit |
| Spezies-Reaktivität: | human, mouse |
707,00 €
Anti-IVD
Artikelnummer: E-AB-18718.120
IVD(Isovaleryl CoA dehydrogenase,mitochondrial) is a member of the acylCoA dehydrogenase family and is involved in the catabolism of leucine. In size,IVD precursor and mature proteins produced by class I mutants are indistinguishable from their normal counterparts. Class II,III,and IV mutants make IVD precursor...
| Schlagworte: | Anti-IVD, EC=1.3.8.4, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial, IVD Polyclonal Antibody |
| Anwendung: | WB, ELISA |
| Wirt: | Rabbit |
| Spezies-Reaktivität: | human, mouse, rat |
ab 89,00 €
Anti-IVD
Artikelnummer: ATA-HPA041391.100
Protein function: Catalyzes the conversion of isovaleryl-CoA/3-methylbutanoyl- CoA to 3-methylbut-2-enoyl-CoA as an intermediate step in the leucine (Leu) catabolic pathway (PubMed:7640268). To a lesser extent, is also able to catalyze the oxidation of other saturated short-chain acyl-CoA thioesters as...
| Schlagworte: | Anti-IVD, Anti-Butyryl-CoA dehydrogenase, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial |
| Anwendung: | ICC, IHC, WB |
| Wirt: | Rabbit |
| Spezies-Reaktivität: | human |
491,00 €
IVD Protein, Mouse, Recombinant (His)
Artikelnummer: TGM-TMPY-05066-100ug
Description: IVD (Isovaleryl-CoA Dehydrogenase) is a Protein Coding gene. IVD is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. IVD plays an essential role in processing proteins obtained from the diet. The body breaks down proteins from food into smaller parts called amino acids....
| Schlagworte: | AI463340, 6720455E18Rik, 1300016K07Rik, isovaleryl-CoA dehydrogenase |
| MW: | 45.3 kD |
768,00 €
NEU
IVD Protein, Human, Recombinant (aa 30-423, His)
Artikelnummer: TGM-TMPY-03264-10ug
Description: IVD Protein, Human, Recombinant (aa 30-423, His) is expressed in Baculovirus Insect Cells. The predicted molecular weight is 45.3 kDa and the accession number is P26440.
| Schlagworte: | Butyryl-CoA dehydrogenase , Isovaleryl-CoA dehydrogenase |
| MW: | 45.3 kD |
ab 75,00 €
NEU
IVD Protein, Mouse, Recombinant (His)
Artikelnummer: TGM-TMPY-05066-5ug
Description: IVD (Isovaleryl-CoA Dehydrogenase) is a Protein Coding gene. IVD is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. IVD plays an essential role in processing proteins obtained from the diet. The body breaks down proteins from food into smaller parts called amino acids....
| Schlagworte: | 6720455E18Rik , AI463340 , isovaleryl-CoA dehydrogenase , 1300016K07Rik |
| MW: | 45.3 kD |
ab 75,00 €
Isovaleryl-DL-carnitine-d9 (chloride)
Artikelnummer: Cay37213-1
Isovaleryl-DL-carnitine-d9 is intended for use as an internal standard for the quantification of isovaleryl-DL-carnitine by GC- or LC-MS. Isovaleryl-DL-carnitine is a derivative of carnitine (Cay-21489, Cay-16749). Increased levels of isovaleryl carnitine are associated with isovaleric acidemia, an inborn error of...
| Schlagworte: | DL-Isovalerylcarnitine-d9, 3-carboxy-N,N,N-tris(methyl-d3)-2-((3-methylbutanoyl)oxy)propan-1-aminium, monochloride |
| Anwendung: | GC-MS, LC-MS internal standard, quantification, isovaleryl-CoA dehydrogenase defiency marker |
| CAS | 2608872-54-2 |
| MW: | 290.8 D |
ab 163,00 €
Anti-IVD
Artikelnummer: ABS-KC-36717.100
Protein function: Catalyzes the conversion of isovaleryl-CoA/3-methylbutanoyl- CoA to 3-methylbut-2-enoyl-CoA as an intermediate step in the leucine (Leu) catabolic pathway (PubMed:7640268). To a lesser extent, is also able to catalyze the oxidation of other saturated short-chain acyl-CoA thioesters as...
| Schlagworte: | Anti-IVD, Anti-Butyryl-CoA dehydrogenase, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial |
| Wirt: | Mouse |
| Spezies-Reaktivität: | human |
ab 232,00 €
Anti-IVD
Artikelnummer: ABS-KC-36230.100
Protein function: Catalyzes the conversion of isovaleryl-CoA/3-methylbutanoyl- CoA to 3-methylbut-2-enoyl-CoA as an intermediate step in the leucine (Leu) catabolic pathway (PubMed:7640268). To a lesser extent, is also able to catalyze the oxidation of other saturated short-chain acyl-CoA thioesters as...
| Schlagworte: | Anti-IVD, Anti-Butyryl-CoA dehydrogenase, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial |
| Wirt: | Mouse |
| Spezies-Reaktivität: | human |
ab 232,00 €