L-Cystine

L-Cystine is a dimeric form of cysteine that is formed by the covalent oxidative linkage of two cysteine residues. It accumulates in the lysosomes of patients with cystinosis, an autosomal recessive lysosomal storage disorder, and is associated with renal Fanconi syndrome and loss of glomerular function.CAS Number: 56-89-3. Synonyms: (-)-Cystine, NSC 13203. Molecular Formula: C6H12N2O4S2. Formula Weight: 240.3. Purity: >95%. Formulation: (Request formulation change), A crystalline solid. SMILES: OC([C@@H](N)CSSC[C@H](N)C(O)=O)=O. InChi Code: InChI=1S/C6H12N2O4S2/c7-3(5(9)10)1-13-14-2-4(8)6(11)12/h3-4H,1-2,7-8H2,(H,9,10)(H,11,12)/t3-,4-/m0/s1. InChi Key: LEVWYRKDKASIDU-IMJSIDKUSA-N.