Anti-PEX19, NT (PEX19, HK33, PXF, Peroxisomal biogenesis factor 19, 33kD housekeeping protein, Perox

Anti-PEX19, NT (PEX19, HK33, PXF, Peroxisomal biogenesis factor 19, 33kD housekeeping protein, Perox
Item number Size Datasheet Manual SDS Delivery time Quantity Price
039892.200 200 µl - -

1 - 19 business days

557.00€
 
This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone... more
Product information "Anti-PEX19, NT (PEX19, HK33, PXF, Peroxisomal biogenesis factor 19, 33kD housekeeping protein, Perox"
This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants. Applications: Suitable for use in Western Blot, ELISA, Recommended Dilution: ELISA: 1:1,000, Western Blot: 1:100-500, Storage and Stability: May be stored at 4°C for short-term only. Aliquot to avoid repeated freezing and thawing. Store at -20°C. Aliquots are stable for 12 months. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.
Keywords: Anti-HK33, Anti-PEX19, Anti-Peroxin-19, Anti-33 kDa housekeeping protein, Anti-Peroxisomal farnesylated protein, Anti-Peroxisomal biogenesis factor 19
Supplier: United States Biological
Supplier-Nr: 039892

Properties

Application: ELISA, WB
Antibody Type: Polyclonal
Conjugate: No
Host: Rabbit
Reactivity: Human
Immunogen: PEX19 antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 32-61 amino acids from the N-terminal region of human PEX19.
Format: Affinity Purified

Handling & Safety

Storage: -20°C
Shipping: +4°C (International: +4°C)
Caution
Our products are for laboratory research use only: Not for administration to humans!
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