Lysosomal Acid Lipase Activity MaxSpec(R) Assay Kit

Lysosomal Acid Lipase Activity MaxSpec(R) Assay Kit
Artikelnummer Größe Datenblatt Manual SDB Lieferzeit Menge Preis
Cay24854-1 1 each -

6 - 10 Werktage*

368,00 €
 
Lysosomal acid lipase (LAL) is a lysosomal enzyme that hydrolyzes cholesteryl esters and... mehr
Produktinformationen "Lysosomal Acid Lipase Activity MaxSpec(R) Assay Kit"
Lysosomal acid lipase (LAL) is a lysosomal enzyme that hydrolyzes cholesteryl esters and triglycerides to produce cholesterol, glycerol, and free fatty acids. LAL deficiency is due to mutations in the LAL gene, LIPA, that lead to decreases in LAL activity. Wolman's disease is a severe form of LAL deficiency that begins in infancy and is characterized by a nearly complete or complete lack of LAL activity resulting in gastrointestinal disorders, hepatomegaly, and failure to thrive, leading to hypercholesterolemia and fatality within months without treatment. Cholesterol ester storage disorder is a less severe form of LAL deficiency in which LAL activity is reduced but not abolished. It presents later in life and is characterized by gastrointestinal disturbances, dyslipidemia, hepatomegaly, and impaired liver function. Research towards development of methods to detect deficiency in this enzyme has become an important goal in diagnosing and treating individuals with this disorder.Synonyms: LAL.
Schlagworte: LAL
Hersteller: Cayman Chemical
Hersteller-Nr: 24854

Eigenschaften

Anwendung: LC-MS/MS, fluorometry, LAL activity determination

Datenbank Information

KEGG ID : K01052 | Passende Produkte

Handhabung & Sicherheit

Lagerung: -20°C
Versand: -20°C (International: -20°C)
Signalwort: Danger
GHS-Piktogramme:
H-Sätze: H225, H319, H336
P-Sätze: P210, P233, P240, P241, P242, P243, P261, P264, P271, P280, P303+361+353, P304+340, P305+351+338, P312, P337+313, P370+378, P403+233, P403+235, P405, P501
Achtung
Nur für Forschungszwecke und Laboruntersuchungen: Nicht für die Anwendung im oder am Menschen!
Hier kriegen Sie ein Zertifikat
oder , um Analysenzertifikate anzufordern.
Bewertungen lesen, schreiben und diskutieren... mehr
Kundenbewertungen für "Lysosomal Acid Lipase Activity MaxSpec(R) Assay Kit"
Bewertung schreiben
oder , um eine Produktbewertung abzugeben.
Zuletzt angesehen